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Progress in Medical Sciences ISSN: 2577 - 2996
Progress in Medical Sciences. 2021; 5(2):(73-83)


A Giant Fibrosarcoma of Gall bladder - A Rare Presentation- A Case Report

Preeti Vijayakumaran, Shravan Nadkarni, Swapnil Patel*, Ipsita Dhal, Mayank Tripathi and Durgatosh Pandey

Abstract
Introduction: Primary gall bladder sarcoma (PGBS) is a rare histopathological diagnosis with uncertainties regarding management. Evidence is available only in the form of anecdotal reports.


Case Description: A 57-year lady presented to our centre with upper abdominal pain and a palpable mass in the right hypochondrium. CT scan revealed a distended gallbladder with a mass in the gallbladder. Repeated Gall bladder biopsy was inconclusive of malignancy, and workup revealed no other evidence of distant metastasis. In view of the massively enlarged gallbladder with corroborating clinical symptoms, cholecystectomy with liver wedge excision and periportal lymph nodal sampling was performed. The histopathological and immunohistochemical evaluation confirmed the diagnosis of a primary gall bladder sarcoma. The patient recovered well and has received adjuvant chemotherapy. 

Conclusion: A rare histological diagnosis masquerading gallbladder cancer may present as a clinical surprise. These rare histologies ought to be reported to help in the timely management of curable diagnostic dilemmas.